Female patient with non-compact myocardium


DOI: https://dx.doi.org/10.18565/therapy.2019.6.176-182

Sayfutdinov R.G., Pak E.V., Sayfutdinov R.R., Rubanova E.F., Garin A.A., Suslov D.A., Iskhakov T.D., Abdrashitov K.M., Kurshakov A.A., Makarimova K.Sh.

1) Kazan state medical Academy – branch of Russian medical Academy of continuing professional education of the Ministry of Healthcare of Russia; 2) Autonomous Public Healthcare Institution «Republican clinical hospital No. 2» of the Ministry of Healthcare of the Republic of Tatarstan
The article discusses the clinical case of a non-compact myocardium (spongy myocardium, noncompaction myocardium) – a very rare form of congenital cardiomyopathy that occurs both in adults and children. It is characterized by excessive trabecularity with deep intertrabular spaces formation. Multiple trabeculaes form a wide non-compact spongy layer of the heart muscle, while a layer of a homogeneous contraction-capable myocardium remains thin. Such an altered structure of the heart muscle leads to a rapidly increasing deterioration of the contractility of the heart and the development in some cases of severe heart failure.
Keywords: spongy myocardium, non-compact myocardium, diagnosis, treatment
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About the Autors

Rafik G. Sayfutdinov, MD, professor, head of the Department of hospital and outpatient therapy of Kazan State medical Academy – a branch of Russian medical Academy of continuing professional education of the Ministry of Healthcare of Russia. Address: 420012, Kazan, 36 Butlerova Str. Tel.: +7 (843) 267-61-51. E-mail: rgsbancorp@mail.ru
Emilia V. Pak, PhD, assistant of the Department of hospital and outpatient therapy of Kazan State medical Academy – a branch of Russian medical Academy of continuing professional education of the Ministry of Healthcare of Russia. Address: 420012, Kazan, 36 Butlerova Str. Tel.: +7 (843) 267-61-51.
Rinat R. Sayfutdinov, PhD, associate professor of the Department of hospital and outpatient therapy of Kazan State medical Academy – a branch of Russian medical Academy of continuing professional education of the Ministry of Healthcare of Russia. Address: 420012, Kazan, 36 Butlerova Str. Tel.: +7 (843) 267-61-51. E-mail: r_saifutdinov@mail.ru
Evelina F. Rubanova, PhD, assistant of the Department of hospital and outpatient therapy of Kazan State medical Academy – a branch of Russian medical Academy of continuing professional education of the Ministry of Healthcare of Russia. Address: 420012, Kazan, 36 Butlerova Str. Tel.: +7 (843) 267-61-51.
Anton A. Garin, head of the Department of therapy of the Autonomous Public Healthcare Institution «Republican clinical hospital No. 2» of the Ministry of Healthcare of the Republic of Tatarstan. Address: 420012, Kazan, 36 Butlerova Str. Tel.: +7 (843) 267-61-51.
Denis A. Suslov, Doctor of the intensive care unit of the Autonomous Public Healthcare Institution «Republican clinical hospital No. 2» of the Ministry of Healthcare of the Republic of Tatarstan. Address: 420012, Kazan, 36 Butlerova Str. Tel.: +7 (843) 267-61-51.
Timur D. Iskhakov, Doctor of functional diagnostics of the Autonomous Public Healthcare Institution «Republican clinical hospital No. 2» of the Ministry of Healthcare of the Republic of Tatarstan. Address: 420012, Kazan, 36 Butlerova Str. Tel.: +7 (843) 267-61-51.
Kamil M. Abdrashitov, pathologist at the of the Autonomous Public Healthcare Institution «Republican clinical hospital No. 2» of the Ministry of Healthcare of the Republic of Tatarstan. Address: 420012, Kazan, 36 Butlerova Str. Tel.: +7 (843) 267-61-51.
Andrei A. Kurshakov, PhD, assistant of the Department of hospital and outpatient therapy of Kazan State medical Academy – branch of Russian medical Academy of continuing professional education of the Ministry of Healthcare of Russia. Address: 420012, Kazan, 36 Butlerova Str. Tel.: +7 (843) 267-61-51. E-mail: kurshan@list.ru
Kamila S. Makarimova, resident of the Department of hospital and outpatient Therapy, Kazan State medical Academy – branch of Russian medical Academy of continuing professional education of the Ministry of Healthcare of Russia. Address: 420012, Kazan, 36 Butlerova Str. Tel.: +7 (843) 267-61-51. E-mail: makamilla@yandex.ru


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