Still’s disease in adults: Methodological recommendations for general practitioners, therapists


DOI: https://dx.doi.org/10.18565/therapy.2023.1.108-115

Mazurov V.I., Trofimov E.A., Gaidukova I.Z., Trofimova A.S.

I.I. Mechnikov North-Western State Medical University of the Ministry of Healthcare of Russia, Saint Petersburg
Abstract. Adult Still’s disease is a rare multisystem autoinflammatory pathology of unknown nature (a special form of seronegative rheumatoid arthritis) characterized by daily sudden rises in body temperature above 39 °C, arthralgia or arthritis, rapidly disappearing skin rash, leukocytosis with a predominance of neutrophils. Article presents modern viewpoints about clinic, diagnosis, and treatment of this autoinflammatory disease.

Literature


1. Клиническая ревматология. Руководство для врачей. 3-е издание, переработанное и дополненное. Под ред. В.И. Мазурова. М.: Е-ното. 2021; 696 с. [Clinical rheumatology. Guide for doctors. 3rd edition, revised and enlarged. Ed. by Mazurov V.I. Moscow: E-noto. 2021; 696 pp. (In Russ.)]. ISBN: 978-5-906023-26-1.


2. Тактика врача-ревматолога: практическое руководство. Под ред. В.И. Мазурова. Москва: ГЭОТАР-Медиа. 2022; 320 с. ил. (Серия «Тактика врача»). [Tactics of a rheumatologist: a practical guide. Ed. by Mazurov V.I. Moscow: GEOTAR-Media. 2022; 320 pp. (Series «Doctor’s Tactics» (In Russ.)]. https://dx.doi.org/10.33029/9704-6824-1-ТOR-2022-1-320. EDN: RFJSLM. ISBN: 978-5-9704-6824-1.


3. Чичкова Н.В., Сулимов В.А., Щедрина И.С., Арутюнян Г.К. Болезнь Стилла взрослых: особенности клинического течения и трудности диагностики. РМЖ. Медицинское обозрение. 2015; 23(17): 1057–1059. [Chichkova N.V., Sulimov V.A., Shchedrina I.S., Harutyunyan G.K. Still’s disease in adults: clinical features and diagnostic difficulties. Russkiy meditsinskiy zhurnal = Russian Medical Journal. Medical Review. 2015; 23(17): 1057–1059 (In Russ.)]. EDN: UJEWBN.


4. Муравьев Ю.В., Лебедева В.В. Болезнь Стилла взрослых в настоящее время. Научно-практическая ревматология. 2017; 55(3): 272–276. [Muravyov Yu.V., Lebedeva V.V. Still’s disease is an adult now. Nauchno-prakticheskaya revmatologiya = Scientific and Practical Rheumatology. 2017; 55(3): 272–276 (In Russ.)]. https://dx.doi.org/10.14412/1995-4484-2017-272-276. EDN: ZGZBRP.


5. Имаметдинова Г.Р., Чичасова Н.В. Болезнь Стилла взрослых: клинические случаи. Современная ревматология. 2014; 8(4): 39–42. [Imametdinova G.R., Chichasova N.V. Still’s disease of adults: clinical cases. Sovremennaya revmatologiya = Modern rheumatology. 2014; 8(4): 39–42 (In Russ.)]. EDN: TAKCNF.


6. Yamaguchi M., Ohta A., Tsunematsu T. et al. Preliminary criteria for classification of adult Still’s disease. J Rheumatol. 1992; 19(3): 424–30.


7. Cush J.J. Adult-onset Still’s disease. Bull Rheum Dis. 2000; 49(6): 1–4.


8. Fautrel B., Zing E., Colmard J.L. et al. Proposal for a new set of classification criteria for adult-onset still disease. Medicine (Baltimor). 2002; 81(3): 194–200. https://dx.doi.org/10.1097/00005792-200205000-00003.


9. Eurofever Classification Criteria. URL: https://www.printo.it/eurofever/scoreCriteria.asp (date of access – 07.04.2020).


About the Autors


Vadim I. Mazurov, MD, professor, academician of RAS, Chief scientific consultant, director of the Research Institute of Rheumatology and head of the Department of therapy, rheumatology, examination of temporary disability and quality of medical care named after E.E. Eichwald, I.I. Mechnikov North-Western State Medical University of the Ministry of Healthcare of Russia, head of the Center for autoimmune diseases of Clinical Rheumatology Hospital No. 25 (Saint Petersburg), Honored Worker of Science of the Russian Federation. Address: 191014, Saint Petersburg, 41 Kirochnaya Str. E-mail: maz.nwgmu@yandex.ru. ORCID: https://orcid.org/0000-0002-0797-2051
Evgeny A. Trofimov, MD, deputy director of the Research Institute of Rheumatology and professor of the Department of therapy, rheumatology, examination of temporary disability and quality of medical care named after E.E. Eichwald, I.I. Mechnikov North-Western State Medical University of the Ministry of Healthcare of Russia. Address: 191014, Saint Petersburg, 41 Kirochnaya Str. E-mail: evgeniy.trofimov@szgmu.ru.
ORCID: https://orcid.org/0000-0003-3236-4485. SPIN-code: 4358-1663
Inna Z. Gaydukova, MD, professor, deputy director of the Research Institute of Rheumatology and professor of the Department of therapy, rheumatology, examination of temporary disability and quality of medical care named after E.E. Eichwald, I.I. Mechnikov North-Western State Medical University of the Ministry of Healthcare of Russia, врач-ревматолог СПб ГБУЗ «Клиническая ревматологическая больница №25». rhemautologist at Clinical Rheumatology Hospital No. 25 (Saint Petersburg). Address: 191014, Saint Petersburg, 41 Kirochnaya Str. E-mail: ubp1976@list.ru. ORCID: https://orcid.org/0000-0003-3500-7256. SPIN-code: 3083-7996
Anna S. Trofimova, PhD in Medical Sciences, assistant at the Department of therapy, rheumatology, examination of temporary disability and quality of medical care named after E.E. Eichwald, I.I. Mechnikov North-Western State Medical University of the Ministry of Healthcare of Russia. Address: 191014, Saint Petersburg, 41 Kirochnaya Str. E-mail: anna.trofimova@szgmu.ru. ORCID: https://orcid.org/0000-0001-5926-7912. SPIN-code: 6827-3934


Бионика Медиа