Clinical diagnosis of Ehlers – Danlos syndromes: new classification criteria for 2017


DOI: https://dx.doi.org/10.18565/therapy.2018.6.121-127

E.L. Trisvetova

Belarusian state medical university, 2nd Department of internal medicine, Minsk
Ehlers-Danlos syndromes (SED) as a manifestation of hereditary disorders of the connective tissue are distinguished by the multisystem damage and the variability of symptoms. The diagnostic criteria developed in 1998, which include the description of 6 types of SED, were successfully used for two decades. However, the results of clinical observation, biochemical and molecular studies are supplemented with new knowledge about the syndrome. New international classification of 2017 contains the diagnostic criteria of 13 types of SED, also hyper-mobile type features are revised there.
Keywords: Ehlers-Danlos syndrome, clinical diagnosis, large and small criteria

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  • About the Autors


    Evgenia L. Trisvetova, MD, professor of the 2nd Department of internal diseases of the educational institution «Belarusian state medical university». 220116, Belarus, Minsk, 83 Pr. Dzerzhinskogo Str. Tel.: +70172771201. E-mail: trisvet-47@mail.ru


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