Acute disorders of cerebral circulation in persons with differentiated connective tissue dysplasias


DOI: https://dx.doi.org/10.18565/therapy.2021.5.88-95

Pizova N.V., Pizov N.A., Skachkova O.A., Shadrichev V.A.

Yaroslavl State Medical University of the Ministry of Healthcare of Russia
Abstract. Acute cerebrovascular accidents (ACVA) are common diseases in people of different sex and age. The causes of ACVA are different and deviate depending on age groups. Currently, there is an increase of stroke incidence in young patients. At a young age, ACVA can develop in persons with congenital connective tissue disorders. Such typical hereditary connective tissue diseases as Marfan syndrome, Ehlers–Danlos syndrome, Lois–Dietz syndrome and elastic pseudoxanthoma are considered thoroughly. The diagnostic criteria for these diseases, data on their prevalence and peculiarities of concomitant ACVA are presented.
Keywords: elastic pseudoxanthoma, Lois–Dietz syndrome, acute cerebral circulation disorders, Ehlers–Danlos syndrome, hereditary connective tissue diseases, Marfan syndrome
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About the Autors

Natalia V. Pizova, MD, professor of the Department of nervous diseases with medical genetics and neurosurgery, Yaroslavl State Medical University of the Ministry of Healthcare of Russia. Address: 150030, Yaroslavl, 39 Suzdal`skoe Highway. E-mail: pizova@yandex.ru. ORCID: 0000-0002-7465-0677
Nikolay A. Pizov, postgraduate student of the Department of nervous diseases with medical genetics and neurosurgery, Yaroslavl State Medical University of the Ministry of Healthcare of Russia. Address: 150030, Yaroslavl, 39 Suzdal`skoe Highway. ORCID: 0000-0002-3009-3020
Olga A. Skachkova, postgraduate student of the Department of nervous diseases with medical genetics and neurosurgery, Yaroslavl State Medical University of the Ministry of Healthcare of Russia. Address: 150030, Yaroslavl, 39 Suzdal`skoe Highway. ORCID: 0000-0001-6825-1322
Vladimir A. Shadrichev, assistant of the Department of nervous diseases with medical genetics and neurosurgery, Yaroslavl State Medical University of the Ministry of Healthcare of Russia. Address: 150030, Yaroslavl, 39 Suzdal`skoe Highway. ORCID: 0000-0002-2340-007X


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