Polycystic liver and kidney disease


DOI: https://dx.doi.org/10.18565/therapy.2022.10.130-135

Mukhametova D.D., Odintsova A.Kh., Kirshin A.A., Kirshina A.R., Khasanshina A.Yu., Garaeva A.R., Mardanov I.A., Abdulganieva D.I.

1) Kazan State Medical University of the Ministry of Healthcare of Russia; 2) Republican Clinical Hospital of the Ministry of Healthcare of the Republic of Tatarstan, Kazan; 3) Kazan (Volga region) Federal University
Abstract. Article presents two clinical observations of patients with associated polycystic liver and kidney disease. Their peculiarity is the presence of clinical manifestations of the disease, which, according to the literature data, is rare. Both cases had a family history of polycystic liver and kidney disease. Onset of illness in example No. 1 occurred at 76 years of age, in example No. 2 – at 44 years of age. At the same time, a different outcome of the disease was fixed – with the development of portal hypertension in the first case and the need for bisegmentotomy in the second. Both patients were included in the waiting list for liver transplantation.
Keywords: polycystic liver disease, polycystic kidney disease, clinical case
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About the Autors

Dilyara D. Mukhametova, PhD in Medicine, assistant at the Department of hospital therapy, Kazan State Medical University of the Ministry of Healthcare of Russia. Address: 420012, Kazan, 49 Butlerova Str. E-mail: muhdilyara@gmail.com. ORCID: https://orcid.org/0000-0003-2102-0142
Alfiya K. Odintsova, PhD in Medicine, head of the gastroenterology Department of Republican Clinical Hospital of the Ministry of Healthcare of the Republic of Tatarstan. Address: 420064, Kazan, 138 Orenburgsky tract Str. E-mail: odincovaa@yandex.ru. ORCID: https://orcid.org/0000-0002-7148-8862
Alexander A. Kirshin, head of the surgical Department No. 2 of Republican Clinical Hospital of the Ministry of Healthcare of the Republic of Tatarstan, assistant at the Department of surgical diseases of postgraduate education of the Institute of fundamental medicine and biology, Kazan (Volga region) Federal University. Address: 420064, Kazan, 138 Orenburgsky tract Str. E-mail: kirshinalex80@mail.ru. ORCID: https://orcid.org/0000-0002-3322-4284
Aigul R. Kirshina, gastroenterologist at the Department of gastroenterology, Republican Clinical Hospital of the Ministry of Healthcare of the Republic of Tatarstan. Address: 420064, Kazan, 138 Orenburgsky tract Str. E-mail: aygulraisovna@gmail.com. ORCID: https://orcid.org/0000-0003-4952-0122
Alina Yu. Khasanshina, gastroenterologist at the Department of gastroenterology, Republican clinical hospital of the Ministry of Healthcare of the Republic of Tatarstan. Address: 420064, Kazan, 138 Orenburgsky tract Str. E-mail: alinahasanshina86@gmail.com. ORCID: https://orcid.org/0000-0002-7716-8106
Alina R. Garaeva, resident of the Department of hospital therapy, Kazan State Medical University of the Ministry of Healthcare of Russia. Address: 420012, Kazan, 49 Butlerova Str. E-mail: alina-garaeva97@mail.ru. ORCID: https://orcid.org/0000-0002-8254-652X
Iskander A. Mardanov, surgeon at the Department of surgery No. 2, Republican Clinical Hospital of the Ministry of Healthcare of the Republic of Tatarstan. Address: 420064, Kazan, 138 Orenburgsky tract Str. E-mail: icmar007@mail.ru. ORCID: https://orcid.org/0000-0002-3171-1660
Diana I. Abdulganieva, Dr. med. habil., professor, head of the Department of hospital therapy, Republican Clinical Hospital of the Ministry of Healthcare of the Republic of Tatarstan. Address: 420012, Kazan, 49 Butlerova Str. E-mail: diana_s@mail.ru. ORCID: https://orcid.org/0000-0001-7069-2725


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