A clinical case of chronic cardiac insufficiency on the background of transthyretin amyloid cardiomyopathy


DOI: https://dx.doi.org/10.18565/therapy.2019.4.121-127

Svanadze A.M., Krylova N.S., Poteshkina N.G., Khadzegova A.B.

1) Faculty of continuing professional education of N.I. Pirogov Russian National research medical University of the Ministry of Healthcare, Moscow; 2) City clinical hospital No 52 of Moscow Department of Healthcare; 3) City clinical hospital No 40 of Moscow Department of Healthcare
The prevalence of amyloidosis has not yet been studied due to undiagnosed cases. Transthyretin amyloidosis is a rare disease, a variant of the family of hereditary amyloidosis, which manifests only in mid-life with a clinical picture of severe chronic heart failure without a prior history of cardiac disease. Presented clinical case illustrates the course of chronic heart failure in patient with transthyretin amyloid cardiomyopathy.
Keywords: treatment transthyretin amyloid cardiomyopathy, transthyretin amyloidosis, congestive heart failure, amyloid cardiomyopathy
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About the Autors

Anna M. Svanadze, PhD, associate professor of the Department of general therapy of Continuous professional education Faculty of N.I. Pirogov Russian scientific medical University of the Ministry of Healthcare of Russia, physician of ultrasound diagnostics of City clinical hospital No 52 of Moscow Department of Healthcare. Address: 123182, Moscow, 3 Pekhotnaya str. Tel.: +7 (916) 958-65-50. E-mail: asvanadze@mail.ru
Natalia S. Krylova, PhD, associate professor of the Department of general therapy of Continuous professional education Faculty of N.I. Pirogov Russian scientific medical University of the Ministry of Healthcare of Russia, physician of functional diagnostics of City clinical hospital No 52 of Moscow Department of Healthcare. Address: 123182, Moscow, 3 Pekhotnaya str.
Natalia G. Poteshkina, MD, professor, the Head of the Department of general therapy of Continuous professional education Faculty of N.I. Pirogov Russian scientific medical University of the Ministry of Healthcare of Russia, therapist, consultant of City clinical hospital No 52 of Moscow Department of Healthcare. Address: 123182, Moscow, 3 Pekhotnaya str.
Alla B. Khadzegova, MD, professor of the Department of general therapy of Continuous professional education Faculty of N.I. Pirogov Russian scientific medical University of the Ministry of Healthcare of Russia, physician of functional diagnostics of City clinical hospital No 40 of Moscow Department of Healthcare. Address: 123182, Moscow, 3 Pekhotnaya str.


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