Clinical case of arrhythmogenic right ventricular dysplasia in pregnant woman


DOI: https://dx.doi.org/10.18565/therapy.2020.1.121-128

Mravyan S.R., Kovalenko T.S., Fedorova S.I.

1) Moscow regional scientific research obstetrics/gynecology institute (MONIAG); 2) Moscow regional research and clinical institute (MONIKI)
А clinical case of arrhythmogenic right ventricular dysplasia (ARVD) in a pregnant woman, the manifestation of which were morphological signs of replacement of cardiomyocytes with fibrous-fatty tissue and lesions of the right ventricle, revealed by magnetic resonance imaging, is presented. From the beginning of clinical manifestations of the disease to pregnancy, the progression of heart muscle lesions was revealed, manifested by the appearance of typical markers of ARVD on the electrocardiogram and the deterioration of the contractility of the right ventricular. The possibility of achieving a satisfactory antiarrhythmic effect on the background of sotalol use is presented. Even with continuing arrhythmia, up to short runs of ventricular tachycardia, pregnancy and childbirth in ARVD occur without complications.
Keywords: right ventricular, arrhythmogenic right ventricular dysplasia, cardiomyopathy, pregnancy
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About the Autors

Sergey R. Mravyan, MD, PhD, leading researcher of physiological obstetric Department of Moscow regional scientific research obstetrics/gynecology institute (MONIAG). Address: 127006, Moscow, 9/88 Krasnoproletarskaya Str.
Tel.: +7 (495) 623-28-47. E-mail: sergeymrav@list.ru. ORCID: orcid.org/0000-0002-9591-8433
Tatiana S. Kovalenko, PhD, senior researcher of physiological obstetric Department of Moscow regional scientific research obstetrics/gynecology institute (MONIAG). Address: 101100, Moscow, 22a Pokrovka Str.
Tel.: +7 (495) 623-28-47. ORCID: orcid.org/0000-0001-8995-6727
Svetlana I. Fedorova, PhD, head of functional diagnostics Department of Moscow regional research and clinical institute (MONIKI). Address: 129110, Moscow, 61/2 Schepkina Str. Tel.: +7 (499) 681-55-71. ORCID: orcid.org/0000-0003-2957-3403


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